pISSN 2234-3806eISSN 2234-3814
Table. 2.
Risk stratification based on the three diagnostic scoring systems for the prediction of TMA due to severe ADAMTS13 deficiency
| Scoring system | Number of risk groups | Risk category | Patients, N (%) | ||
|---|---|---|---|---|---|
| TMA (–) | TMA (+) | ||||
| FTMA-S | Three | L | 7 (6.9) | 0 (0.0) | 0.006 |
| I | 48 (47.5) | 12 (27.3) | |||
| H | 46 (45.6) | 32 (72.7) | |||
| Two | L–I | 55 (54.5) | 12 (27.3) | 0.003 | |
| H | 46 (45.5) | 32 (72.7) | |||
| PLASMIC-S | Three | L | 49 (48.5) | 2 (4.5) | < 0.001 |
| I | 34 (33.7) | 6 (13.6) | |||
| H | 18 (17.8) | 36 (81.8) | |||
| Two | L–I | 83 (82.2) | 8 (18.2) | < 0.001 | |
| H | 18 (17.8) | 36 (81.8) | |||
| B-S | Three | L | 94 (93.1) | 35 (79.6) | 0.055 |
| I | 5 (4.9) | 7 (15.9) | |||
| H | 2 (2.0%) | 2 (4.5%) | |||
| Two | L–I | 99 (98.0) | 42 (95.5) | 0.585 | |
| H | 2 (2.0) | 2 (4.5) | |||
*
Abbreviations: TMA, thrombotic microangiopathy; ADAMTS13, a disintegrin and metalloprotease with thrombospondin type 1 motif, member 13; FTMA-S, French TMA score; PLASMIC-S, PLASMIC score; B-S, BENTLEY score; L, low risk; I, intermediate risk; H, high risk.
Ann Lab Med 2023;43:485~492 https://doi.org/10.3343/alm.2023.43.5.485
© Ann Lab Med